cutaneous necrotizing vasculitis
Cutaneous necrotizing vasculitis (CNV) is a complex multisystem disease generally involving the skin and mucous membranes, often accompanied by renal, gastrointestinal, pericardial, neurological, and articular signs and symptoms.
CNV may be idiopatical or occur in association with a drug, infection, or underlying disease.
Associations
chronic infections (viral, bacterial, protozoa, helminthic)
serum sickness
collagen vascular diseases (systemic lupus erythematous, Sjögren?s syndrome, rheumatoid arthritis, Behçet?s disease)
hyperglobulinemic states cryoglobulinemia bowel bypass syndrome ulcerative colitis cystic fibrosis primary biliary cirrhosis HIV infection.
malignancies -* lymphoproliferative disorders
- Hodgkin disease
- mycosis fungoides
- lymphomas
- adult T-cell leukemia
- multiple myeloma)
solid tumors
- lung cancer
- colon carcinoma
- renal, prostate, head and neck cancer and breast cancer
See also
vasculitis
References
Lotti TM, Comacchi C, Ghersetich I.Cutaneous necrotizing vasculitis. Relation to systemic disease.Adv Exp Med Biol. 1999;455:115-25. PMID: 10599332