systemic granulomatoses
Etiology:
infectious systemic granulomatoses
- tuberculosis
- atypical mycobacteriosis
- Mycobacterium kansasii
- Mycobacterium avium intracellualre (MAI)
systemic tuberculoid granulomatoses
- chronic familial granulomatosis
- sarcoidosis
- necrotizing sarcoid granulomatosis
- Crohn disease
- familial juvenile systemic granulomatosis (FJGS) (Blau syndrome) (CARD15 mutations)
systemic necrotizing granulomatosis
Wegener granulomatosis
Churg-Strauss angiitis
tumoral systemic granulomatoses
systemic histiocytoses
- langerhans histiocytosis
- non-Langerhans cell histiocytoses
- Erdheim-Chester disease
- systemic juvenile xanthogranuloma
- necrobiotic xanthogranuloma
- adult disseminated xanthoma
constitutional immune deficiencies
miscellaneous
- lipogranulomatoses
- hyalinizing plasmacytic granulomatosis (2451439)
- familial juvenile systemic granulomatosis (FJSG)
Localization
tracheal granulomatosis
pulmonary granulomatosis
renal granulomatosis
splenic granulomatosis
digestive granulomatosis
Types
necrotizing granulomatosis
tuberculoid granulomatosis (sarcoid granulomatosis)
familial systemic granulomatosis
See also
- tuberculoid granuloma
- epithelioid granuloma
References
Schuetz C, Huck K, Gudowius S, Megahed M, Feyen O, Hubner B, Schneider DT, Manfras B, Pannicke U, Willemze R, Knüchel R, Göbel U, Schulz A, Borkhardt A, Friedrich W, Schwarz K, Niehues T. An immunodeficiency disease with RAG mutations and granulomas. N Engl J Med. 2008 May 8;358(19):2030-8. PMID: 18463379





