Spindle cell haemangioendothelioma is an entirely benign, non-recurring lesion which has been renamed spindle cell hemangioma.
Similarly, it is now appreciated that as many as 20–30% of epithelioid haemangioendotheliomas may give rise to distant metastases (albeit the rate is lower in cytologically bland examples) and hence these tumours have been redesignated as malignant.
Intermediate vascular tumours are now subcategorized into locally aggressive and rarely metastasizing subsets.
Associations
Maffucci syndrome
varicose veins
congenital lymphedema
Differential diagnosis
Kaposi sarcoma
angiosarcoma
Return to: vascular tumors
References
The evolving classification of soft tissue tumours: an update based on the new WHO classification. Fletcher CD. Histopathology. 2006 Jan;48(1):3-12. PMID: 16359532