Sclerosing cholangitis can be primary (PSC) or secondary.
Subtypes
primary sclerosing cholangitis (PSC)
- neonatal sclerosing cholangitis
- auto-immune sclerosing cholangitis
secondary sclerosing cholangitis (SSC)
- infectious chronic cholangitis
- biliary cryptosporidiosis (immunodeficiencies)
- Langerhans cell histiocytosis
- choledocholithiasis
- sickle cell disease
- total parenteral nutrition
- Hodgkin disease
- primary intestinal T-cell lymphoma (9893108)
- cystic fibrosis
- postbiliary surgery
- ischemia (floxuridine)
- IgG4-associated sclerosing cholangitis
-
genetic diseases
- ichtyosis and scarring alopecia
- kabuki mask syndrome
- Lawrence-Moon-Bardet-Bield syndrome (BBS)
Associations
immunodeficiencies
- hyper-IgM syndrome
- AIDS-related cholangiopathy
- post-liver transplantation