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sclerosing cholangitis

Wednesday 4 June 2003

Sclerosing cholangitis can be primary (PSC) or secondary.

Subtypes

- primary sclerosing cholangitis (PSC)

  • neonatal sclerosing cholangitis
  • auto-immune sclerosing cholangitis

- secondary sclerosing cholangitis (SSC)

  • Langerhans cell histiocytosis
  • choledocholithiasis
    • sickle cell disease
    • total parenteral nutrition
  • Hodgkin disease
  • primary intestinal T-cell lymphoma (9893108)
  • cystic fibrosis
  • postbiliary surgery
  • ischemia (floxuridine)
  • IgG4-associated sclerosing cholangitis
  • genetic diseases
    • ichtyosis and scarring alopecia
    • kabuki mask syndrome
    • Lawrence-Moon-Bardet-Bield syndrome (BBS)

Associations

- immunodeficiencies

  • hyper-IgM syndrome
  • AIDS-related cholangiopathy
  • post-liver transplantation

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