congenital pulmonary lymphangiectasis
congenital pulmonary lymphangiectases
Examples
unilobar congenital pulmonary lymphangiectasis (UCPL) (15136998)
Associations
Ivemark syndrome with asplenia
- total anomalous pulmonary venous connection (TAPVC)
- atrioventricular communis
- septal defects
cardiovascular malformations
- total anomalous pulmonary venous connection (TAPVC)
- aortic arch malformation
- hypoplastic left heart (left heart hypoplasia)
- atrioventricular communis
- ventricular septal defect (VSD)
congenital lobar emphysema (4715376, 5936105)
renal malformations
ichtyosis congenita
cystic fibrosis
generalized lymphangioma
omphalocele (exomphalos)
See also
pulmonary lymphangiectases
References
Chapdelaine J, Beaunoyer M, St-Vil D, Oligny LL, Garel L, Bütter A, Di Lorenzo M. Unilobar congenital pulmonary lymphangiectasis mimicking congenital lobar emphysema: an underestimated presentation? J Pediatr Surg. 2004 May;39(5):677-80. PMID: 15136998