Humpath.com - Human pathology

Home > E. Pathology by systems > Respiratory system > Lungs > congenital pulmonary lymphangiectasis

congenital pulmonary lymphangiectasis

Thursday 6 December 2007

Types

- CPL, Noonan Group 1
- CPL, Noonan Group 2
- CPL, Noonan Group 3
- unilobar congenital pulmonary lymphangiectasis (UCPL) (15136998)

Associations

- Ivemark syndrome with asplenia

- cardiovascular malformations

- congenital lobar emphysema (4715376, 5936105)
- renal malformations
- ichtyosis congenita
- cystic fibrosis
- generalized lymphangioma
- omphalocele (exomphalos)

See also

- pulmonary lymphangiectases

References

- Congenital pulmonary lymphangiectasis: report of an autopsy case masquerading as pulmonary interstitial emphysema. Yamada S, Hisaoka M, Hamada T, Araki S, Shiraishi M. Pathol Res Pract. 2010 Jul 15;206(7):522-6. PMID: 20399027

- Chapdelaine J, Beaunoyer M, St-Vil D, Oligny LL, Garel L, B├╝tter A, Di Lorenzo M. Unilobar congenital pulmonary lymphangiectasis mimicking congenital lobar emphysema: an underestimated presentation? J Pediatr Surg. 2004 May;39(5):677-80. PMID: 15136998