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nevus lipomatosus superficialis

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Nevus lipomatosus superficialis
nevus lipomatosus cutaneous superficialis, Hoffmann-Zurhelle

Nevus lipomatosus superficialis (NLS) is a rare benign cutaneous hamartoma characterized by papules and nodules usually in the pelvic and sacral areas, with ectopic mature adipose tissue reaching the superficial dermis.

Associations

- multiple folliculosebaceous cystic hamartomas (FCH) (15649197)
- dermoid cysts (15649197)
- perifollicular fibrosis (14721781)
- basal cell carcinoma (12786865)
- cavernous hemangioma (3074101)

Cytogenetics

- 2p24 deletion (17223884)

See also

- Skin

Cardot-Leccia N, Italiano A, Monteil MC, Basc E, Perrin C, Pedeutour F. Naevus lipomatosus superficialis: a case report with a 2p24 deletion. Br J Dermatol. 2007 Feb;156(2):380-1. PMID: 17223884