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colonic cystic fibrosis

Macroscopical synopsis

- meconial plug
- colonic obstruction (meconium ileus equivalent)(6630579)
- colonic perforation (1974979)

- colonic wall thickening (increase wall thickness)
- stenosis (fibrosing colonopathy) after pancreatic enzyme supplementation or not (12352527)
- colonic strictures (7596943)
- colonic diverticulitis causing partial bowel obstruction (9388282)
- mebeverine-induced perforated colon (1971070)
- cystic fibrosis-associated colonopathy
- fibrosing colonopathy
- cystic fibrosis-associated colitis

Microscopical synopsis

- uniform dilatation of glands containing inspissated mucin and prominent goblet cells (hypercrinia)

- local wall fibrosis (fibrosing colonopathy) (11840048)

  • after pancreatic enzyme supplementation
  • without pancreatic enzyme supplementation not (12352527)

- diffuse wall fibrosis (9388282)
- ulcerative colitis (7596655)

Variants

- cystic fibrosis colonopathy

Keywords