Types
total anomalous pulmonary venous connection to a systemic vein (58% of patients with visceral heterotaxy and asplenia)
partial anomalous pulmonary venous connection to a systemic vein (3%)
anomalous pulmonary venous connection with obstruction (55%)
cardiac pulmonary venous connections
- pulmonary veins and inferior vena cava entering the same atrium
pulmonary venous obstruction
Associations
abnormal pulmonary artery branches
- severe hypoplasia
- localized stenosis
- discontinuity
obstructive pulmonary arterial anomalies
anomalous pulmonary venous connection
See also
anomalous venous connections
- anomalous systemic venous connection
Associations
heterotaxy
- situs ambiguus
Case records
Case 10300