anomalous pulmonary venous connections

Total anomalous pulmonary venous connection Total anomalous pulmonary venous connection Total anomalous pulmonary venous connection

Types

- total anomalous pulmonary venous connection to a systemic vein (58% of patients with visceral heterotaxy and asplenia)
- partial anomalous pulmonary venous connection to a systemic vein (3%)
- anomalous pulmonary venous connection with obstruction (55%)
- cardiac pulmonary venous connections

  • pulmonary veins and inferior vena cava entering the same atrium
    - pulmonary venous obstruction

Associations

- abnormal pulmonary artery branches

  • severe hypoplasia
  • localized stenosis
  • discontinuity
    - obstructive pulmonary arterial anomalies
    - anomalous pulmonary venous connection

See also

- anomalous venous connections

  • anomalous systemic venous connection

Associations

- heterotaxy

  • situs ambiguus

Case records

- Case 10300

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