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PNPT1

polynucleotide phosphorylase, PNPase, OLD35, polyribonucleotide nucleotidyltransferase 1

Definition: PNPT1 is a subunit of the exosome complex, which is involved in 3-prime-to-5-prime exoribonuclease activity for RNA processing and degradation.

Human polynucleotide phosphorylase (hPNPase) is an RNA-processing enzyme induced in response to type I interferons and during terminal differentiation and cellular senescence.

hPNPase was thought to contribute to cellular senescence through its RNA-degrading activity in the cytosol.

However, hPNPase localizes to the mitochondrial intermembrane space (IMS) and has a crucial role in maintaining mitochondrial homeostasis. Initial studies have also linked hPNPase to tumorigenesis and the cellular response to viral infection.

References

- Chen HW, Koehler CM, Teitell MA. Human polynucleotide phosphorylase: location matters. Trends Cell Biol. 2007 Dec;17(12):600-8. PMID: 17983748