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Home > E. Pathology by systems > Urinary system > Kidneys > renal cystic dysplasia

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renal cystic dysplasia

IMG/jpg/renal_adysplasia_05_1-3.jpg IMG/jpg/renal_adysplasia_05_2-3.jpg

Renal dysplasia is defined as abnormal metanephric differentiation.

Classification

- bilateral obstructive renal cystic dysplasia

  • lower urinary tract obstruction

- non-obstructive bilateral renal cystic dysplasia

  • nonsyndromal cystic renal dysplasia
    • sporadic nonsyndromal cystic renal dysplasia
    • familial nonsyndromal cystic renal dysplasia
    • isolated renal Meckel syndrome
    • partial trisomy resulting from parental unbalanced translocation
  • syndromal renal dysplasia (malformative syndromes - multisystem maldevelopment)
    • Meckel syndrome
    • Zellweger syndrome
    • autosomic recessive polycystic kidney disease (ARPKD) with hepato-pancreato-renal dysplasia
    • Jeune syndrome