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nephronophthisis-associated liver disease

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Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Normal portal space and interlobular biliary ducts in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...) Portal fibrosis and biliary ductular proliferation in juvenile (...)
congenital hepatic fibrosis-nephronophthisis, nephronophthisis-associated congenital hepatic fibrosis

Synopsis

- +/- ductal plate malformation (nephronophthisis-associated congenital hepatic fibrosis)
- +/- portal inflammation
- +/- portal fibrosis

See also

- medullary cystic kidney diseases (MCKDs)

  • nephronophthisis

References

- Johnson CA, Gissen P, Sergi C. Molecular pathology and genetics of congenital hepatorenal fibrocystic syndromes. J Med Genet. 2003 May;40(5):311-9. PMID: 12746391

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