Human pathology

Home page > D. Systemic pathology > Genetic and developmental anomalies > juvenile hyaline fibromatosis

juvenile hyaline fibromatosis

puretic syndrome

Etiology

- Juvenile hyaline fibromatosis (JHF) is caused by germline mutation in the gene encoding capillary morphogenesis protein-2 (CMG2) (MIM.608041) at locus 4q21

Differential diagnosis

- infantile systemic hyalinosis (15690301)