Definition: Extralobar pulmonary sequestration (ELPS) are segmentsof lung tissue ("accessory lungs") with a distinct pleural investment and complete anatomic and physiologic seprartion from the normal lung. Blood supply is usually by anomalous systemic artery with venous drainage into the azygos or hemizygos system.
The abnormal tissue may be located either above or below the diaphragm, most often on the left side.
Localization
right extralobar pulmonary sequestration (10%)
left extralobar pulmonary sequestration (90%)
infradiaphragmatic extralobar pulmonary sequestration
variants
bronchopulmonary sequestration supplied from the renal artery (2326448)
Associations
congenital cystic adenomatoid malformation (CCAM) (10441623)
- inside CCAM
- outside CCAM
renal anomalies
diaphragmatic hernia
malformative syndrome
- association anomalous pulmonary venous return, pulmonary sequestration, bronchial atresia, aplastic right upper lobe, pericardial defect and intrathoracic kidney (5944198)
Case records
See also
thoracic malformations
pulmonary malformations