dermatomyositis
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Synopsis
dermatomyositis-associated cardiomyopathy
dermatomyositis-associated immune-complex type glomerulonephritis
dermatomyositis-associated vasculitis
- dermatomyositis-associated cutaneous arteriolitis
Muscle biopsy
periodic acid Schiff- (PAS) positive vacuoles
infiltrates of mononuclear cells
reduced phosphorylase activity
Biology
anti-mitochondrial antibody
mitochondrial anomalies
- perifascicular atrophic fibers
cytochrome c oxidase (COX)
succinate dehydrogenase (SDH)
mitochondrial dysfunction in perifascicular distribution (15614615)
abnormal SDH and COX histochemical activities in atrophic perifascicular fibers (15614615)