cutaneous reactive angiomatose
Types
cutaneous reactive angioendotheliomatosis
acroangiodermatitis (pseudo-Kaposi sarcoma)
diffuse dermal angiomatosis
intravascular histocytosis
glomeruloid angioendotheliomatosis
angiopericytomatosis (angiomatosis with cryoproteins)
Synopsis
propensity to involve limbs
macroscopy
- multiple, erythematous-violaceous
- purpuric patches
- purpuric plaques
- necrosis
- ulceration
- intravascular or extravascular
- lobular pattern
- diffuse pattern
- hyperplasia of endothelial cells, pericytes, and sometimes histiocytes
Differential diagnosis
vascular tumors
References
Rongioletti F, Rebora A. Cutaneous reactive angiomatoses: patterns and classification of reactive vascular proliferation. J Am Acad Dermatol. 2003 Nov;49(5):887-96. PMID: 14576670