Autosomal recessive malformative disease.
Synopsis
short stature (<25th percentile)
obesity
brachycephaly
midface hypoplasia
low-set ears
malformed ears
preauricular pits
conductive hearing loss
sensorineural hearing loss
epicanthal folds
corneal opacity
microcornea
optic atrophy
lateral displacement of medial canthi
flat nasal bridge
high-arched palate
missing teeth
delayed loss of deciduous teeth
short muscular neck
atrial septal defect
ventricular septal defect
pulmonic stenosis
tetralogy of Fallot
transposition of great vessels
patent ductus arteriosus
umbilical hernia
omphalocele
accessory spleens
cryptorchidism
hydronephrosis
hydroureter
craniosynostoses
- oronal craniosynostosis
- sagittal craniosynostosis
- lambdoid sutures craniosynostosis
pilonidal dimple
absent coccyx
spina bifida occulta
scoliosis
coxa valga
decreased hip-joint mobility
flared ilia
genu valgum
lateral displacement of patellae
brachydactyly
hand postaxial polydactyly
clinodactyly
hand syndactyly
camptodactyly
foot preaxial polydactyly
foot syndactyly
metatarsus varus
variable delay (IQ range 52-104)
precocious puberty
See also
acrocephalopolysyndactylies
- acrocephalopolysyndactyly type 1 (ACPS1)