Human pathology

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SHANK3

MIM.606230 22q13.3

Pathology

- SHANK3 mutation in 22q13.3 deletion syndrome (MIM.606232)

References

- Moessner R, Marshall CR, Sutcliffe JS, Skaug J, Pinto D, Vincent J, Zwaigenbaum L, Fernandez B, Roberts W, Szatmari P, Scherer SW.Contribution of SHANK3 Mutations to Autism Spectrum Disorder.Am J Hum Genet. 2007 Dec;81(6):1289-97. PMID: 17999366

- Wilson, H. L.; Wong, A. C. C.; Shaw, S. R.; Tse, W.-Y.; Stapleton, G. A.; Phelan, M. C.; Hu, S.; Marshall, J.; McDermid, H. E. : Molecular characterisation of the 22q13 deletion syndrome supports the role of haploinsufficiency of SHANK3/PROSAP2 in the major neurological symptoms. J. Med. Genet. 40: 575-584, 2003. PubMed ID : 12920066

- Wong, A. C. C.; Ning, Y.; Flint, J.; Clark, K.; Dumanski, J. P.; Ledbetter, D. H.; McDermid, H. E. : Molecular characterization of a 130-kb terminal microdeletion at 22q in a child with mild mental retardation. Am. J. Hum. Genet. 60: 113-120, 1997. PubMed ID : 8981954