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PKLR

Pyruvate kinase (PKs) (ATP:pyruvate phosphotransferase) (EC 2.7.1.40) is a glycolytic enzyme that catalyzes the transfer of a phosphoryl group from phosphoenolpyruvate (PEP) to ADP, generating ATP.

Pathology

- PKLR germline mutations in pyruvate kinase deficiency (MIM.266200)

See also

- PKs (pyruvate kinases)