Kasabach-Merritt syndrome
consumptive coagulopathy
Definition: Kasabach-Merritt phenomenon (KMP) is characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, a consumptive coagulopathy, and an enlarging vascular lesion.
Kasabach-Merritt phenomenon is a serious coagulopathy associated with kaposiform hemangioendothelioma (KHE), tufted angioma, and possibly other vascular neoplasms.
Classification
vascular tumors
- kaposiform hemangioendothelioma
- tufted angioma
- multifocal lymphangioendotheliomatosis with thrombocytopenia (15148106)
- angiosarcoma (12410374, 17505172)
- angioblastoma (9764180)
vascular dysplasias
fibrosarcoma (14726860)