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Hedgehog-signaling related diseases

Hh-signaling related diseases

Classification

- holoprosencephaly (SHH, PTCH)
- Pallister-Hall syndrome (GLI3)
- Grieg cephalopolysyndactyly (GLI3)
- post-axial polydactyly type 3 (GLI3)
- VACTERL (GLI2 and GLI3)
- Rubinstein-Taybi syndrome
- nevoid basal cell carcinoma syndrome (PTCH)
- sporadic basal cell carcinoma (PTCH)
- sporadic basal cell carcinoma (SMO)
- sporadic medulloblastoma (PTCH)
- Smith-Lemli-Opitz disease (DHCR7)
- glioblastoma (GLI1)

References

- Pasca di Magliano M, Hebrok M. Hedgehog signalling in cancer formation and maintenance.Nat Rev Cancer. 2003 Dec;3(12):903-11. PMID: 14737121

- Bale AE, Yu KP. The hedgehog pathway and basal cell carcinomas. Hum Mol Genet. 2001 Apr;10(7):757-62. PMID: 11257109