C4a deficiency
MIM.120810 6p21.3
C4 deficiency
Associations
Wegener granulomatosis (8296646)
Henoch-Schönlein purpura (8296646)
References
Lhotta K, Kronenberg F, Joannidis M, Feichtinger H, König P. Wegener’s granulomatosis and Henoch-Schönlein purpura in a family with hereditary C4 deficiency. Adv Exp Med Biol. 1993;336:415-8. PMID: 8296646