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C1 inhibitor deficiency-associated systemic lupus erythematosus

C1 inhibitor deficiency-associated SLE, Systemic lupus erythematosus with C1q deficiency, Lupus erythematosus associated with C1 inhibitor deficiency

Synopsis

- cutaneous lupus
- Raynaud phenomenon
- non-scarring alopecia
- oral ulceration
- cerebral vasculitis (10735963)

References

- Koide M, Shirahama S, Tokura Y, Takigawa M, Hayakawa M, Furukawa F. Lupus erythematosus associated with C1 inhibitor deficiency. J Dermatol. 2002 Aug;29(8):503-7. PMID: 12227484

- Stone NM, Williams A, Wilkinson JD, Bird G. Systemic lupus erythematosus with C1q deficiency. Br J Dermatol. 2000 Mar;142(3):521-4. PMID: 10735963