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autoimmune enteric leiomyositis

Wednesday 9 November 2005

Autoimmune enteric leiomyositis (AIELM) is an extraordinary rare cause of acquired chronic intestinal pseudo-obstruction in children.

Synopsis

- acquired chronic intestinal pseudoobstruction (acquired CIPO)
- dense lymphocytic infiltrate of the muscularis propria

  • mainly consisting of cytotoxic T lymphocytes

- smooth muscle fibers degenerated and diminished
- myenteric plexus intact
-  mucosa and submucosa without severe inflammatory changes

Associations

- autoimmune hepatitis
- gastritis
- colitis

See also

- enteric leiomyositis

References

- Haas S, Bindl L, Fischer HP. Autoimmune enteric leiomyositis: a rare cause of chronic intestinal pseudo-obstruction with specific morphological features. Hum Pathol. 2005 May;36(5):576-80. PMID: 15948126

- Ruuska TH, Karikoski R, Smith VV, et al. Acquired myopathic intestinal pseudo-obstruction may be due to autoimmune enteric leiomyositis. Gastroenterology 2002; 122:1133-1139.