pulmonary vasculitis

Types according to lesional pattern

 granulomatous vasculitis

• Wegener granulomatosis
• Churg-Strauss angiitis and granulomatosis
• giant cell arteritis (Horton arteritis)
• disseminated visceral giant cell angiitis
• bronchocentric granulomatosis
• necrotizing sarcoid granulomatosis
• granulomatous infections
  • mycobacterial infections (e.g. tuberculosis)
  • fungal infections (e.g. histoplasmosis)

Types according to the etiology

 ’idiopathic’ pulmonary vasculitis

• Wegener granulomatosis
• Churg-Strauss disease (eosinophilic angiitis and granulomatosis)
• microscopic polyangiitis

Types according to frequency

 idiopathic vasculitis syndromes that commonly affect the lung

• Wegener granulomatosis
• Churg-Strauss angiitis and granulomatosis
• microscopic polyangiitis

 idiopathic vasculitis syndromes that commonly affect the lung

• necrotizing sarcoid granulomatosis
• polarteritis nodosa
• small vessel vasculitis
• Takayasu arteritis
• Henoch-Schõnlein purpura
• Behcet syndrome
• cryoglobulinemic vasculitis
• hypocomplementemic vasculitis
• idiopathic granulomatous vasculitis
  • giant cell arteritis (Horton arteritis)
  • disseminated visceral giant cell angiitis

 miscellaneous systemic disorders

• classic sarcoidosis
• collagen vascular disease
• inflammatory bowel disease
• malignancy

 diffuse pulmonary hemorrhage syndrome

 secondary or localized vasculitis

• pulmonary infection
• bronchiocentric granulomatosis
• pulmonary hypertension
• interstitial lung diseases
  • chronic eosniphilic pneumonia
  • Langerhans cell histiocytosis

• inflammatory pseudotumors
• sequestration
• embolic material (intravenous drug abuse0
• drugs
• toxic substance
• transplantation
• radiation

 vascular involvment in lymphoproliferative disorders

• lymphomatoid granulomatosi (angiocentric immunoproliferative lesion)
• non-Hodgkin lymphoma
• intravascular malignant lymphoma