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intestinal lymphangiectasia

Monday 7 July 2003

Ent. Waldman, 1961

Images

- Small intestine polyp. Secondary Lymphangiectasia

Synopsis

- loss of chylous fluid into the gut lumen
- chylous ascite, chylous pleural effusions
- protein-losing enteropathy syndrome

  • lymphopenia
  • hypogammaglobulinaemia

Etiology

- primitive intestinal lymphangiectasia (congenital obstructive defects of the digestive lymphatics) (Waldmann disease)

- primitive intestinal lymphangiectasia in other genetic diseases

  • aplasia cutis (MIM.207731)
  • Hennekam lymphangiectasia (MIM.235510)

- secondary intestinal lymphagiectasia

  • lymph node obstruction
  • acute inflammation
  • infectious enteritis
  • intestinal fibrosis
  • intraluminal precipitates
  • extraluminal compression
  • lymph node infiltration
  • increased thoracic duct pressure

See also

- lymphatic anomalies

  • digestive lymphatic anomalies