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fibromatoses

Monday 1 March 2004

Digital case

- JRC:11438 : Superficial fibromatosis (Juvenile, digital) (NOS)

Definition: Fibromatoses are rare soft tissue disease characterized by fibroblastic proliferation.

Classification

- fibroblastic fibromatoses

  • desmoid fibromatosis (desmoid tumor, aggressive fibromatosis)
  • fibromatosis colli
  • digital infantile fibromatosis
  • aponevrotic fibromatosis
    • plantar fibromatosis
    • palmar fibromatosis
    • penile fibromatosis
  • hereditary gingival fibromatosis (idiopathic gingival fibromatosis)
  • lipofibromatosis

- myofibroblastic fibromatoses (myofibromatoses)

  • infantile myofibromatosis (infantile myofibroma)

According to the localization

- superficial fibromatoses
- deep fibromatoses

See also

- fibrous tumors
- fibroblastic tumors

References

- Montgomery E, Lee JH, Abraham SC, Wu TT. Superficial fibromatoses are genetically distinct from deep fibromatoses. Mod Pathol 2001 Jul;14(7):695-701

- Allen PW. The fibromatoses: a clinicopathologic classification based on 140 cases. Am J Surg Pathol. 1977 Sep;1(3):255-70.