ERCCs
Members
| ERCC1 | ERCC2 | ERCC3 | ERCC4 | ERCC5 | ERCC6 | ERCC7 | ERCC8 |
Pathology
ERCC1 (MIM.126380)
- cerebrooculofacioskeletal syndrome locus 4 (COFS4) (MIM.610758)
ERCC2 (MIM.)
- xeroderma pigmentosum complementation group D (MIM.278730)
- trichothiodystrophy (TTD) (MIM.601675)
- cerebrooculofacioskeletal syndrome locus 2 (COFS2) (MIM.610756)
ERCC3 (MIM.133510)
- type B xeroderma pigmentosum/Cockayne syndrome (MIM.610651)
- Cockayne syndrome
- trichothiodystrophy (TTD) (MIM.601675)
ERCC4 (MIM.133520)
- xeroderma pigmentosum complementation group F (XPF) (278760)
- xeroderma pigmentosum complementation group E (XPE) with progeroid syndrome (MIM.610965)
ERCC5 (MIM.133530)
- xeroderma pigmentosum complementation group G (MIM.278780)
- severe early-onset XPG/Cockayne syndrome (MIM.278780)
- Cockayne syndrome
ERCC6 (MIM.133540)
- Cockayne syndrome type B (MIM.133540)
- cerebrooculofacioskeletal syndrome (COFS syndrome) (MIM.214150)
- UV-sensitive syndrome (MIM.600630)
ERCC8 (MIM.609412)
- Cockayne syndrome type A (MIM.216400)