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congenital soft tissue dysplasias
Wednesday 12 November 2003
The term congenital soft tissue dysplasias (CSTDs) regroups some localized malformations of covering soft tissues in children, presenting as various clinical entities.
Classification
Parkes-Weber syndrome
Klippel-Trenaunay syndrome
Proteus syndrome
segmental hypertrophy (segmental gigantism)
lymphedema
angiodysplasia
Synopsis
giant hamartoma
angiodysplasia
congenital hypertrophy
congenital trophoedema
localised gigantism
- macrodactyly
References
Martelli H, Richard S, Moczar M, Godeau G, Pfister A, Pellerin D, Vekemans M. Congenital soft tissue dysplasias: a morphological and biochemical study. Pediatr Pathol. 1994 Sep-Oct;14(5):873-94.
PMID: 7808985
Pellerin D, Martelli H, Latouche X, Couly G, Gasnier F. Congenital soft tissue dysplasia: a new malformation entity and concept. Prog Pediatr Surg. 1989;22:1-29. PMID: 2492383
