Home > A. Molecular pathology > globosides
globosides
Wednesday 30 July 2008
Lipids > sphingolipids > glycosphingolipids > globosides
Definition: A globoside is a type of glycosphingolipid (containing amino-alcohol sphingosine) with N-Acetylgalactosamine as the side chain.
The side chain can be cleaved by beta-hexosaminidase.
Pathology
If the enzyme beta-hexosaminidase is not functioning correctly (gene mutation), then globosides can accumulate, leading to Sandhoff disease.
See also
- glycosphingolipids (amino alcohol sphingosine)
- cerebrosides
- gangliosides
- globosides