pulmonary sequestration and congenital pulmonary airway malformation

Digital cases (Digital slides)

 HPC:370 : Cystic congenital adenomatoid malformation in extrapulmonary sequestration
 HPC:413 : Cystic congenital adenomatoid malformation in extralobar pulmonary sequestration

Definition: Association of an extralobar pulmonary sequestration and a CPAM.

Types

 extralobar sequestration

• congenital cystic adenomatoid malformation type 2 within a extralobar sequestration (8516226)
• congenital cystic adenomatoid malformation (CCAM or CPAM) connected to an extralobar pulmonary sequestration in the contralateral chest (15300558)
• congenital cystic adenomatoid malformation and extralobar sequestration in the ipsilateral hemithorax (10663851)
• intra-abdominal pulmonary sequestration associated with congenital cystic adenomatoid malformation of the lung (9587942, 7944891)
• extralobar sequestration, type II congenital cystic adenomatoid malformation, and congenital diaphragmatic hernia (9025860)

 intralobar seuestration

• intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia (14551713)
• intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia. Pediatr Surg Int. 2003 Oct;19(8):610-1. PMID: 14551713

References

 McLean SE, Pfeifer JD, Siegel MJ, Jensen ER, Schuler PM, Hirsch R, Mychaliska GB. Congenital cystic adenomatoid malformation connected to an extralobar pulmonary sequestration in the contralateral chest: common origin? J Pediatr Surg. 2004 Aug;39(8):e13-7. PMID: 15300558

 Orpen N, Goodman R, Bowker C, Lakhoo K. Intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia. Pediatr Surg Int. 2003 Oct;19(8):610-1. PMID: 14551713

 Conran RM, Stocker JT. Extralobar sequestration with frequently associated congenital cystic adenomatoid malformation, type 2: report of 50 cases. Pediatr Dev Pathol. 1999 Sep-Oct;2(5):454-63. PMID: 10441623

See also

 pulmonary malformations