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macrovesicular steatosis

Thursday 24 May 2007

macrovacuolar steatosis

Digital cases

- HPC:402 : Steatosis and hemosiderosis after parenteral nutrition

Etiology

- toxics

  • alcohol (ethanol)
  • phosphore

- drugs

  • corticosteroids
  • bleomycin
  • methotrexate
  • wrafrin
  • zidovudine
  • troglitazone
  • interferon-alpha

- genetic metabolic diseases (inborn errors of metabolism)

  • hereditary fructose intolerance
  • galactosemia
  • glycogenosis type 1 (GSD1)
  • glycogenosis type 3 (GSD3)
  • tyrosinemia
  • Wolman disease
  • cholesterol ester storage disease
  • mitochondrial respiratory chain diseases
  • fatty acid oxydation diseases
  • pyruvate carboxylase deficiency
  • pyruvate dehydrogenase deficiency
  • neonatal adrenoleukodystrophy
  • infantile Refsum disease
  • herediatry tyrosinemia
  • Wilson disease
  • organic acidurias
  • homocystinuria
  • urea cycle diseases
  • Schwachman disease
  • abetalipoproteinemia
  • familial heterozygous hypolipoproteinemia
  • familial hepatosteatosis
  • carnitine-acylcarnitine translocase deficiency

- diabetes mellitus
- obesity
- metabolic syndrome X
- jejunoileal bypass
- starvation
- protein-calorie malnutrtion
- total parenteral nutrition (TPN)
- inflammatory bowel disease (IBDs) (Crohn disease, ulcerous colitis)
- cachexia
- severe anemia
- hyperlipidemia
- hepatitis C infection (VHC infection)
- panhypopituitarism
- malaria
- immotile cilia syndrome

See also

- Steatosis

  • hepatocytic steatosis
    • microvesicular steatosis

- nonalcoholic fatty liver disease (NAFLD)