Home > F. Pathology by regions > Thorax > bronchopulmonary foregut malformation
bronchopulmonary foregut malformation
Friday 24 November 2006
Definition: Bronchopulmonary foregut malformation (BPFM) are segments of sequestered lung tissue, either intralobar or extralobar, that communicate with the alimentary tract, particularly the esophagus.
The bronchopulmonary-foregut malformations (BPFM) are usually sporadic, solitary cystic hamartomas involving conducting airways, arteries, venous drainage, and lung parenchyma. The right side is involved more frequently than the left.
Ventral anomalies of accessory pulmonary tissue have been classified as "bronchopulmonary foregut malformations."
Differential diagnosis
congenital cystic adenomatoid malformation of the lung (CCAML or CPAM).
bronchogenic cyst (BC)
See also
extralobar pulmonary sequestration (ELOS)
References
Newman B. Congenital bronchopulmonary foregut malformations: concepts and controversies. Pediatr Radiol. 2006 Aug;36(8):773-91. PMID: 16552585
Barnes NA, Pilling DW. Bronchopulmonary foregut malformations: embryology, radiology and quandary. Eur Radiol. 2003 Dec;13(12):2659-73. PMID: 14631525
Kousseff BG, Gilbert-Barness E, Debich-Spicer D. Bronchopulmonary-foregut malformations: a continuum of paracrine hamartomas? Am J Med Genet. 1997 Jan 10;68(1):12-7. PMID: 8986269
Rodgers BM, Harman PK, Johnson AM. Bronchopulmonary foregut malformations. The spectrum of anomalies. Ann Surg. 1986 May;203(5):517-24. PMID: 3707230
