communicating bronchopulmonary foregut malformation

Definition: Communicating bronchopulmonary foregut malformations (CBPFM) are a diverse group of potentially devastating congenital anomalies with anatomy that may be difficult to delineate.

Synopsis

 esophageal atresia (EA)
 tracheoesophageal fistula (TEF)
 tetralogy of Fallot (ToF)
 atretic left mainstem bronchus
 left unilobed lung arising from the esophagus
 DiGeorge syndrome

References

 Singal AK, Kumar VR, Rao M, Matthai J. Bilateral communicating bronchopulmonary foregut malformations in a child. Ann Thorac Surg. 2006 Jul;82(1):330-2. PMID: 16798247

 Saydam TC, Mychaliska GB, Harrison MR. Esophageal lung with multiple congenital anomalies: conundrums in diagnosis and management. J Pediatr Surg. 1999 Apr;34(4):615-8. PMID: 10235336