Definition: Clear cell meningioma (CCM) is a rare variant of meningioma. It is rare tumor of the nervous system that usually occur in young patients and display high recurrence rates and potentially aggressive behavior.
Only 17 cases have been previously reported in children. Although it has bland cytologic features, it has a higher rate of recurrence than does conventional meningioma.
Localization
spinal/intradural (lumbar and thoracic)
cerebellopontine angle
supratentorial
orbit (18193452)
Differential diagnosis
microcystic meningioma
hemangioblastoma
clear cell ependymoma
Cytogenetics
References
Benchetritt M, Hofman V, Long E, Odin G, Basc E, Pasquier B, Pedeutour F, Hofman P. Primary clear cell meningioma of the orbit mimicking a metastatic carcinoma: usefulness of immunohistochemistry and cytogenetic analysis.Virchows Arch. 2008 Feb;452(2):209-13. PMID: 18193452
Oviedo A, Pang D, Zovickian J, Smith M. Clear cell meningioma: case report and review of the literature. Pediatr Dev Pathol. 2005 May-Jun;8(3):386-90. PMID: 16010490
