Ebstein's anomaly is a congenital deformity of the tricuspid valve consisting mainly of leaflet malinsertion.

Clinical presentation varies from asymptomatic patients to those with congestive heart failure secondary to significant valvular regurgitation and low right ventricular output.

Synopsis

 Ebstein's deformity of the left-sided tricuspid valve
 pulmonary hypertension
 endocardial fibroelastosis

Associations

 transposition of the great arteries

References

 Dahdah NS, van Doesburg NH, Russo P. Endocardial fibroelastosis in L-transposition of the great arteries with Ebstein's anomaly: revisited. Pediatr Dev Pathol. 1998 Sep-Oct;1(5):427-32. PMID: #9688767#