Autoinflammatory diseases are defined as recurrent "unprovoked" inflammatory events which do not produce high-titer autoantibodies or antigen-specific T cells.

Types

 Familial Mediterranean fever (FMF)
 hyperimmunoglobulinemia D with periodic fever syndrome (HIDS)
 tumor necrosis factor receptor-associated periodic syndrome (TRAPS)
 Muckle-Wells syndrome (MWS)
 familial cold autoinflammatory syndrome (FCAS)
 chronic infantile neurologic cutaneous articular (CINCA) syndrome or neonatal-onset multisystem inflammatory disease (NOMID)
 pyogenic sterile arthritis
 cryopyrin-associated periodic syndrome (CAPS)
 pyoderma gangrenosum
 acne (PAPA)
 familial juvenile systemic granulomatosis (Blau syndrome)
 Crohn disease
 mevalonate kinase deficiency

References

 Tunca M, Ozdogan H. Molecular and genetic characteristics of hereditary autoinflammatory diseases. Curr Drug Targets Inflamm Allergy. 2005 Feb;4(1):77-80. PMID: #15720239#

 Touitou I, Notarnicola C, Grandemange S. Identifying mutations in autoinflammatory diseases: towards novel genetic tests and therapies? Am J Pharmacogenomics. 2004;4(2):109-18. PMID: #15059033#

 McDermott MF, Aksentijevich I. The autoinflammatory syndromes. Curr Opin Allergy Clin Immunol. 2002 Dec;2(6):511-6. PMID: #14752334#