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pelvicaliceal dilatation
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polysplenia
Associations (Exemples)
heterotaxies ans
situs anomalies
visceroatrial
heterotaxy
(
Ivemark syndrome
) (MIM.208530)
Cu
mming type
campomelia
(MIM.211890)
X-linked visceral
heterotaxy
(
ZIC3
mutations)
pulmonary arteriovenous malformation
s
Polysplenia
Polysplenia
Asplenia-Polysplenia in Ivemark syndrome - (From
thefetus.net
)
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