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pulmonary nodular lymphoid hyperplasia

PNLH, pulmonary pseudolymphoma

 

Synopsis

-  expansive and circumscribed nodular lymphoid aggregations along the course of bronchovascular bundles
-  sharp demarcation from normal parenchyma
-  follicular lymphoid hyeprplasia
-  interfollicular lymphoplasmocytosis
-  extension along lobular septa and in interalveolar septa
-  no destructive lymphoepithelial lesions
-  no Dutcher bodies (eosinophilic intranuclear deposits of immunoglobulin)
-  no follicular colonization by atypical lymphocytes

Associations

-  dysimmunity - autoimmune disorders
-  AIDS

Differential diagnosis

-  simple BALT hyperplasia (follicular bronchiolitis)
-  lymphoid interstitial pneumonia (LIP)


Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) with GLILD. BALT hyperplasia. CD20 immunolabeling.

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) with GLILD. BALT hyperplasia. CD20 immunolabeling.

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

Pulmonary nodular lymphoid hyperplasia - Combined variable immunodeficiency (CVID) wilt GLILD

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