Topography

 unilateral multicystic kidney

• unilateral multicystic renal dysplasia

 bilateral multicystic kidneys

• bilateral multicystic renal dysplasia
  • bilateral multicystic obstructive renal dysplasia

Etiology

 urinary obstruction (obstructive kidney)
 genetic diseases

• polycystic kidney diseases
  • ARPKD
  • ADPKD

• genetic metabolic diseases
  • multiple acyl-CoA dehydrogenation deficiency (glutaric aciduria type 2)

Association

 multicystic kidneys and polydactyly

• Bardet-Biel syndrome
• Meckel syndrome
• Pallister-Hall syndrome
• Joubert syndrome
• Jeune syndrome
• Smith-Lemli-Opitz syndrome
• oro-facio-digital I syndrome (OFDI syndrome)
• Simpson-Golabi-behmel syndrome

 multicystic kidneys and ductal plate malformations (DPM)
 corpus callosum agenesis

• BBS

See also

 renal cysts

• monocystic kidney (unique renal cyst)
• oligocystic kidneys