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digestive pneumatosis

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Colonic pneumatosis in infectious colitis Colonic pneumatosis in cystic fibrosis Colonic pneumatosis in cystic fibrosis
pneumatosis cystoides intestinalis

Localization

- intestinal pneumatosis
- colonic pneumatosis

Synopsis

- cryptitis
- crypt abscesses
- mucosal chronic inflammation
- mucosal granulomas
- crypt dilation
- partial crypt rupture
- intramucosal cysts
- clusters of small gas cysts in the lamina propria.

Etiology

- neonatal necrotizing enterocolitis (NNEC)
- anaerobial bacterial enterocolitis
- high intraluminal pressure

  • cystic fibrosis (16702447, 9530294)
  • chronic digestive obstruction
    • adhesional obstruction (16420873)
    • motility disorders (12.5%)
      • sclerodermy (15981628)
      • primary intestinal pseudo-obstruction (16271330)
      • acute colonic pseudo-obstruction (Ogilvie syndrome) (14650951)

Associations

- healthy children (22%)
- organ and bone marrow transplant (22%)
- decompensated congenital heart disease (12.5%)

- gastroschisis (9%)
- short bowel syndrome (6%)

- most common events immediately preceding

  • noninfectious colitis (32%)
  • acute enteric infection or toxin (27%)
  • bowel ischemia (20%)
  • gastrointestinal dysmotility (17%)
  • graft versus host disease colitis

See also

- Pneumatosis

References

- Pieterse AS, Leong AS, Rowland R. The mucosal changes and pathogenesis of pneumatosis cystoides intestinalis. Hum Pathol. 1985 Jul;16(7):683-8. PMID: 4007844