Association of gastric leiomyosarcoma (epithelioid leiomyosarcoma), functioning extraadrenal paraganglioma, and pulmonary chondroma. (The Carney syndrome terminology is avoided because it can be confused with the Carney complex.)

Synopsis

 gastric GIST (gastrointestinal stroma tumors) (ex-gastric leiomyosarcoma) (#15712189#)
 functioning extra-adrenal paragangliomas
 pulmonary chondroma
 nonfunctioning adrenocortical adenoma

Differential diagnosis

 familial paraganglioma and gastric stromal sarcoma association (#11857563#, #15383933#)

References

 Boccon-Gibod L, Boman F, Boudjemaa S, Fabre M, Leverger G, Carney AJ. Separate occurrence of extra-adrenal paraganglioma and gastrointestinal stromal tumor in monozygotic twins: probable familial Carney syndrome. Pediatr Dev Pathol. 2004 Jul-Aug;7(4):380-4. Epub 2004 Jul 15. PMID: #15383933#

 Carney JA. Gastric stromal sarcoma, pulmonary chondroma, and extra-adrenal paraganglioma (Carney Triad): natural history, adrenocortical component, and possible familial occurrence. Mayo Clin Proc. 1999 Jun;74(6):543-52. PMID: #10377927#

 Kiryu T, Kawaguchi S, Matsui E, Hoshi H, Kokubo M, Shimokawa K. Multiple chondromatous hamartomas of the lung: a case report and review of the literature with special reference to Carney syndrome.Cancer. 1999 Jun 15;85(12):2557-61. PMID: #10375102#