pulmonary capillary hemangiomatosis
Capillary proliferations in the pulmonary alveolar walls. Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension.
Synopsis
capillary proliferations in the pulmonary alveolar walls
numerous cytologically benign thin-walled capillary-sized blood vessels proliferating diffusely through alveolar walls and in and around larger vessels and airways
venous infiltration with intimal fibrosis and secondary veno-occlusive disease
Predisposition
hereditary hemorrhagic telangiectasia (HTT) (#14991548#)
References
Tron V, Magee F, Wright JL, Colby T, Churg A. Pulmonary capillary hemangiomatosis. Hum Pathol. 1986 Nov;17(11):1144-50. PMID: #3770733#
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