Classification

 bilateral obstructive renal cystic dysplasia

• lower urinary tract obstruction

 non-obstructive bilateral renal cystic dysplasia

• nonsyndromal cystic renal dysplasia
  • sporadic nonsyndromal cystic renal dysplasia
  • familial nonsyndromal cystic renal dysplasia
  • isolated renal Meckel syndrome
  • partial trisomy resulting from parental unbalanced translocation

• syndromal renal dysplasia (malformative syndromes - multisystem maldevelopment)
  • Meckel syndrome
  • Zellweger syndrome
  • autosomic recessive polycystic kidney disease (ARPKD) with hepato-pancreato-renal dysplasia
  • Jeune syndrome