Subtypes

 primary sclerosing cholangitis

• neonatal sclerosing cholangitis
• auto-immune sclerosing cholangitis

 secondary sclerosing cholangitis

• infectious chronic cholangitis
  • biliary cryptosporidiosis (immunodeficiencies)

• Langerhans cell histiocytosis
• choledocholithiasis
  • sickle cell disease
  • total parenteral nutrition

• Hodgkin disease
• primary intestinal T-cell lymphoma (#9893108#)
• cystic fibrosis
• postbiliary surgery
• ischemia (floxuridine)
• genetic diseases
  • ichtyosis and scarring alopecia
  • kabuki mask syndrome
  • Lawrence-Moon-Bardet-Bield syndrome (BBS)

Associations

 immunodeficiencies

• hyper-IgM syndrome
• AIDS-related cholangiopathy
• post-liver transplantation