Classification

extrahepatic cholestasis

intrahepatic cholestasis

 biliary ducts

• Alagille's syndrome
• Norwegian cholestasis
• neonatal sclerosing cholangitis
• turkish nonsyndromic paucity of interlobular bile ducts
• north american indian cirrhosis (16q22)

 lobule

• congenital anomalies of bile acid metabolism
• progressive familial intrahepatic cholestases (PFIC)
  • PFIC-1 (Byler's disease) (P-type adenosine triphosphatse - 18q21-22)
  • benign recurrent intrahepatic cholestasis (BRIC) (P-type adenosine triphosphatse - 18q21-22)
  • PFIC-2 (Canalicular bile acide transporte ABCB11 - 2q24)
  • PFIC-3 (canalicular phospholipid transporter ABCB4 - 7q21)

 Unknown origin

• Greenland Eskimo cholestasis
• indian childhood cirrhosis
• childhood cirrhosis in Arab israelis
• tyrolean infantile cirrhosis