unilateral pulmonary artery agenesis
UPAA
References
Griffin N, Mansfield L, Redmond KC, Dusmet M, Goldstraw P, Mittal TK, Padley S. Imaging features of isolated unilateral pulmonary artery agenesis presenting in adulthood: a review of four cases. Clin Radiol. 2007 Mar;62(3):238-44. PMID: 17293217