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hepatic Zellweger syndrome

Friday 30 May 2003

Zellweger disease is the most severe of the peroxisome biogenesis disorders. The peroxisome biogenesis disorders are subdivided into 12 complementation groups (CGs).

Synopsis

- absent liver peroxisomes
- intrahepatic biliary dysgenesis
- prolonged neonatal jaundice

See also

- peroxisomal diseases

  • Zellweger disease